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        產(chǎn)品名稱 PMM2, 1-246aa, Human, His tag, E.coli from ATGen
        產(chǎn)品貨號 ATGP0727
        產(chǎn)品價格 現(xiàn)貨詢價,電話:010-67529703
        產(chǎn)品規(guī)格 0.5mg, 100ug, 20ug
        產(chǎn)品品牌 ATGen
        產(chǎn)品概述
        產(chǎn)品詳情
        Edit&nbsp
        Product NamePMM2, 1-246aa, Human, His tag, E.coli
        DescriptionPurity: > 95 % by SDS - PAGE Format: Liquid. In 20mM Tris-HCl buffer(pH 8.0) containing 10% glycerol, 1mM DTT, 0.1M NaCl. . PMM2, also known as Phosphomannomutase 2, belongs to the eukaryotic PMM family. PMM2 is involved in the synthesis of the GDP-mannose and dolichol-phosphate-mannose required for a number of critical mannosyl transfer reactions. It catalyzes the isomerization of mannose 6-phosphate to mannose 1-phosphate. Mutations in PMM2 are associated with Congenital disorders of glycosylation (CDG)-Ia, an autosomal recessive disorder characterized by central nervous system dysfunction and multiorgan failure. Recombinant human PMM2 protein, fused to His-tag at N-terminus, was expressed in E.coli and purified by using conventional chromatography techniques.
        Size0.5mg, 100ug, 20ug
        Concentrationn/a
        ApplicationsSDS-PAGE
        Other NamesPhosphomannomutase 2, CDG1, CDG1a, CDGS, Phosphomannomutase 2
        Gene, Accession, CAS #NP 000294
        Catalog #ATGP0727
        Price
        Order / More InfoPMM2, 1-246aa, Human, His tag, E.coli from ATGen
        Product Specific Referencesn/a
        產(chǎn)品資料
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