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        產(chǎn)品名稱 HMBS, 1-361aa, Human, His tag, E.coli from ATGen
        產(chǎn)品貨號(hào) ATGP1433
        產(chǎn)品價(jià)格 現(xiàn)貨詢價(jià),電話:010-67529703
        產(chǎn)品規(guī)格 0.5mg, 100ug, 20ug
        產(chǎn)品品牌 ATGen
        產(chǎn)品概述
        產(chǎn)品詳情
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        Product NameHMBS, 1-361aa, Human, His tag, E.coli
        DescriptionPurity: > 95% by SDS - PAGE Format: Liquid. In 20mM Tris-HCl buffer (pH 8.0) containing 1mM DTT, 10% glycerol, 0.1M NaCl . Porphobilinogen deaminase, also known as HMBS, is a member of the hydroxymethylbilane synthase superfamily. It is a cytoplasmic enzyme found in the heme synthesis pathway. Deficiency of HMBS causes errors in pyrrole metabolism which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP) which is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine. Recombinant human HMBS protein, fused to His-tag at N-terminus, was expressed in E.coli and purified by using conventional chromatography techniques.
        Size0.5mg, 100ug, 20ug
        Concentrationn/a
        ApplicationsSDS-PAGE
        Other NamesPorphobilinogen deaminase, PBG-D, PBGD, PORC, uPS
        Gene, Accession, CAS #NP 000181
        Catalog #ATGP1433
        Price
        Order / More InfoHMBS, 1-361aa, Human, His tag, E.coli from ATGen
        Product Specific Referencesn/a
        產(chǎn)品資料
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