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        產(chǎn)品名稱 ACOX1 Antibody from BIOSS ANTIBODIES
        產(chǎn)品貨號(hào) bs-5021R
        產(chǎn)品價(jià)格 現(xiàn)貨詢價(jià),電話:010-67529703
        產(chǎn)品規(guī)格 100ul
        產(chǎn)品品牌 BIOSS ANTIBODIES
        產(chǎn)品概述
        產(chǎn)品詳情
        Edit&nbsp
        Antigenic SpecificityACOX1
        Clonepolyclonal
        Host SpeciesRabbit
        Reactive Specieshuman, mouse, rat
        Isotypen/a
        FormatProtein A purified
        Size100ul
        Concentration1ug/ul
        ApplicationsWB, IHC-P, IF(IHC-P)
        Reviews / RatingsIf you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY.
        DescriptionACOX1 Polyclonal Antibody. ? Target Background: Defects in ACOX1 are the cause of adrenoleukodystrophy pseudoneonatal (Pseudo-NALD); also known as peroxisomal acyl-CoA oxidase deficiency. Pseudo-NALD is a peroxisomal single-enzyme disorder. Clinical features include mental retardation, leukodystrophy, seizures, mild hepatomegaly, hearing deficit. Pseudo-NALD is characterized by increased plasma levels of very-long chain fatty cids, due to decreased or absent peroxisome acyl-CoA oxidase activity. Peroxisomes are intact and functioning.
        ImmunogenKLH conjugated synthetic peptide derived from human ACOX1
        Other NamesACOX1; ACOX1_HUMAN; AOX antibody Palmitoyl CoA oxidase; Palmitoyl-CoA oxidase; Peroxisomal acyl coenzyme A oxidase 1; Peroxisomal acyl-coenzyme A oxidase 1; SCOX; Straight chain acyl CoA oxidase; Straight-chain acyl-CoA oxidase.
        Gene, Accession #Gene ID: 51
        Catalog #bs-5021R
        Price
        Order / More InfoACOX1 Antibody from BIOSS ANTIBODIES
        Product Specific Referencesn/a
        產(chǎn)品資料
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