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        產(chǎn)品名稱 ACADSB, 34-432aa, Human, His tag, E.coli from ATGen
        產(chǎn)品貨號(hào) ATGP1628
        產(chǎn)品價(jià)格 現(xiàn)貨詢價(jià),電話:010-67529703
        產(chǎn)品規(guī)格 250ug, 50ug, 10ug
        產(chǎn)品品牌 ATGen
        產(chǎn)品概述
        產(chǎn)品詳情
        Edit&nbsp
        Product NameACADSB, 34-432aa, Human, His tag, E.coli
        DescriptionPurity: > 90% by SDS - PAGE Format: Liquid. In 20mM Tris-HCl buffer (pH 8.0) containing 0.1M NaCl, 10% glycerol,1mM DTT. Short/branched chain specific acyl-CoA dehydrogenase(ACADSB), is a member of the acyl-CoA dehydrogenase family of enzymes that catalyze the dehydrogenation of acyl-CoA derivatives in the metabolism of fatty acids or branch chained amino acids. ACADSB catalyzes the degradation of L-isoleucine and has the highest affinity for (s)-2-methylbutyryl-CoA, isobutyryl-CoA and 2-methylhexanoyl-CoA as substrates. Defects in ACADSB are the cause of short/branched-chain acyl-CoA dehydrogenase deficiency (SBCADD), an autosomal recessive disorder characterized by an increase of 2-methylbutyrylglycine and 2-methylbutyrylcarnitine in blood and urine. Recombinant human ACADSB protein, fused to His-tag at N-terminus, was expressed in E.coli and purified by using conventional chromatography techniques.
        Size250ug, 50ug, 10ug
        Concentrationn/a
        ApplicationsSDS-PAGE
        Other NamesShort/branched chain specific acyl-CoA dehydrogenase mitochondrial, Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial, 2-MEBCAD, ACAD7, SBCAD
        Gene, Accession, CAS #NP 001600
        Catalog #ATGP1628
        Price
        Order / More InfoACADSB, 34-432aa, Human, His tag, E.coli from ATGen
        Product Specific Referencesn/a
        產(chǎn)品資料
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