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        產(chǎn)品名稱 Glucosylsphingosine Analysis from CREATIVE PROTEOMICS
        產(chǎn)品貨號(hào) n/a
        產(chǎn)品價(jià)格 現(xiàn)貨詢價(jià),電話:010-67529703
        產(chǎn)品規(guī)格 n/a
        產(chǎn)品品牌 CREATIVE PROTEOMICS
        產(chǎn)品概述
        產(chǎn)品詳情
        Edit&nbsp
        Product NameGlucosylsphingosine Analysis
        DescriptionGaucher disease is an autosomal recessive lysosomal storage disease caused by a deficiency of glucosylceramidase (β-glucosidase), which results in the abnormal accumulation of glucosylceramide (GlcCer) in tissues. The accumulation of glucosylsphingosine (GlcSph), a derivative of GlcCer devoid of fatty acids, has been demonstrated in the affected tissues of patients with Gaucher disease.
        Sizen/a
        Concentrationn/a
        Applicationsn/a
        Other Namesn/a
        Gene, Accession, CAS #n/a
        Catalog #n/a
        Price
        Order / More InfoGlucosylsphingosine Analysis from CREATIVE PROTEOMICS
        Product Specific Referencesn/a
        產(chǎn)品資料
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