| 產(chǎn)品詳情 |
| Edit |   |
| Antigenic Specificity | MCCC2 |
| Clone | polyclonal |
| Host Species | Rabbit |
| Reactive Species | human, mouse, rat |
| Isotype | n/a |
| Format | immunogen affinity purified |
| Size | 100μg |
| Concentration | n/a |
| Applications | ELISA, WB, IHC ? WB 1:500 - 1:2000; IHC 1:50 - 1:200 |
| Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
| Description | Rabbit anti-MCCC2 polyclonal antibody. This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. |
| Immunogen | methylcrotonoyl-Coenzyme A carboxylase 2 (beta) |
| Other Names | MCCB |
| Gene, Accession # | Gene ID: 64087, UniProt: Q9HCC0 |
| Catalog # | FNab05048 |
| Price | |
| Order / More Info | MCCC2 Antibody from FINETEST |
| Product Specific References | n/a |
| 產(chǎn)品資料 |
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