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        產(chǎn)品名稱 ALDH6A1, 34-535aa, Human, His tag, E.coli from ATGen
        產(chǎn)品貨號 ATGP3087
        產(chǎn)品價格 現(xiàn)貨詢價,電話:010-67529703
        產(chǎn)品規(guī)格 100ug, 20ug, 4ug
        產(chǎn)品品牌 ATGen
        產(chǎn)品概述
        產(chǎn)品詳情
        Edit&nbsp
        Product NameALDH6A1, 34-535aa, Human, His tag, E.coli
        DescriptionPurity: > 85% by SDS - PAGE Format: Liquid, In Phosphate buffered saline (pH7.4) containing 10% glycerol, 1mM DTT. ALDH6A1 also known as Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial. ALDH6A1 is a mitochondrial methylmalonate semialdehyde dehydrogenase that plays a role in the valine and pyrimidine catabolic pathways. This protein catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. ALDH6A1 deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids. Recombinant human ALDH6A1, fused to His-tag at N-terminus, was expressed in E.coli and purified by using conventional chromatography techniques.
        Size100ug, 20ug, 4ug
        Concentrationn/a
        ApplicationsSDS-PAGE
        Other NamesMethylmalonate-semialdehyde dehydrogenase acylating mitochondrial isoform 1, MMSADHA, MMSDH
        Gene, Accession, CAS #NP 005580
        Catalog #ATGP3087
        Price
        Order / More InfoALDH6A1, 34-535aa, Human, His tag, E.coli from ATGen
        Product Specific Referencesn/a
        產(chǎn)品資料
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